BERNARD I. POPHAM, M.D.; THOMAS D. STEVENSON, M.D.
In 1948 Ormond1 described two patients with bilateral hydronephrosis secondary to obstruction of the ureters by retroperitoneal fibrous tissue proliferation of unknown etiology. Since the original description by Ormond, 23 similar cases have been reported in the literature. The clinical manifestations are predominantly the result of ureteral obstruction, with subsequent hydronephrosis and renal infection, or insufficiency due to the involvement of the ureters in the retroperitoneal fibrous tissue reaction. The term "bilateral symmetrical periureteric fibrosis" was used by Raper9 in 1955 to describe this syndrome, but subsequently this same author felt that "idiopathic retroperitoneal fibrosis" was a more suitable appellation.10
POPHAM BI, STEVENSON TD. IDIOPATHIC RETROPERITONEAL FIBROSIS ASSOCIATED WITH A COAGULATION DEFECT (FACTOR VII DEFICIENCY): REPORT OF A CASE AND REVIEW OF THE LITERATURE1. Ann Intern Med. ;52:894–906. doi: 10.7326/0003-4819-52-4-894
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Published: Ann Intern Med. 1960;52(4):894-906.
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