McCluskey DR, Boyd NAM. Prevalence of primary hypogammaglobulinaemia in Northern Ireland. Proc R Coll Physicians Edinb. 1989; 19:191-4.
Fasth A. Primary immunodeficiency disorders in Sweden: cases among children, 1974-1979. J Clin Immunol. 1982; 2:86-92.
Asherson GL. Late-onset hypogammaglobulinemia. In: Asherson GL, Webster AD, eds. Diagnosis and Treatment of Immunodeficiency. London. Blackwell Scientific Publications; 1980:37-60.
Cunningham-Rundles C. Clinical and immunologic analyses of 103 patients with common variable immunodeficiency. J Clin Immunol. 1989; 9:22-33.
Hermans PE, Diax-Buxo JA, Stobo JD. Idiopathic late-onset immunoglobulin deficiency. Clinical observations in 50 patients. Am J Med. 1976; 61:221-36.
Lederman HM, Winkelstein JA. X-linked agammaglobulinemia: an analysis of 96 patients. Medicine. 1985; 64:145-56.
Straus SE, Seidlin M, Takiff H, Jacobs D, Bowen D, Smith HA. Oral acyclovir to suppress recurring herpes simplex virus infections in immunodeficient patients. Ann Intern Med. 1984; 100:522-4.
Freeman HJ, Shnitka TK, Piercey JRA, Weinstein WM. Cytomegalovirus infection of the gastrointestinal tract in a patient with late onset immunodeficiency syndrome. Gastroenterology. 1977; 73:1397- 403.
McKinney RE Jr, Katz SL, Wilfert CM. Chronic enteroviral meningoencephalitis in agammaglobulinemic patients. Rev Infect Dis. 1987; 9:334-56.
Wagner DK, Wright JJ, Ansher AF, Gill VJ. Dysgonic fermenter 3-associated gastrointestinal disease in a patient with common variable hypogammaglobulinemia. Am J Med. 1988; 84:315-8.
Kinlin LJ, Webster ABD, Bird AG, Haile R, Peto J, Soothill JF, et al. Prospective study of cancer in patients with hypogammaglobulinemia. Lancet. 1985; 1:263-6.
Webster ADB, Platts-Mills TAE, Jannossy G, Morgan M, Asherson GL. Autoimmune blood dyscrasias in five patients with hypogammaglobulinemia: response of neutropenia to vincristine. J Clin Immunol. 1981; 1:113-8.
Leickly FE, Buckley RH. Successful treatment of autoimmune hemolytic anemia in common variable immunodeficiency with high-dose intravenous globulin. Am J Med. 1987; 82:159-62.
Twomey JJ, Jordan PH, Jarrold T, Trubowitz S, Ritz ND, Conn HO. The syndrome of immunoglobulin deficiency and pernicious anemia. Am J Med. 1969; 47:340-50.
Cunningham-Rundles C, Siegal FP, Cunningham-Rundles S, Lieberman P. Incidence of cancer in 98 patients with common varied immunodeficiency. J Clin Immunol. 1987; 7:294-9.
Sander CA, Medeiros LJ, Weiss LM, Yano T, Sneller MC, Jaffe ES. Lymphoproliferative lesions in patients with common variable immunodeficiency syndrome. Am J Surg Pathol. 1992; 16:1170-82.
Johnston CL, Webster ABD, Taylor-Robinson D, Rapaport G, Hughes GR. Primary late-onset hypogammaglobulinemia associated with inflammatory polyarthritis and septic arthritis due to Mycoplasma pneumoniae Ann Rheum Dis. 1983; 42:108-10.
Jefferis R, Kumararatne DS. Selective IgG subclass deficiency: quantification and clinical relevance. Clin Exp Immunol. 1990; 81: 357-67.
Ambrosino DM, Siber GR, Chilmonczyk BA, Jernberg JB, Finberg RW. An immunodeficiency characterized by impaired antibody responses to polysaccharides. N Engl J Med. 1987; 316:790-3.
Choi YS, Bigger WD, Good RA. Biosynthesis and secretion of immunoglobulins by peripheral-blood lymphocytes in severe hypogammaglobulinaemia. Lancet. 1972; 1:1149-52.
Wu LYF, Lawton AR, Cooper MD. Differentiation capacity of cultured B lymphocytes from immunodeficient patients. J Clin Invest. 1973; 52:3180-9.
de la Concha EG, Oldham G, Webster ADB, Asherson GL, Platts-Mills TAE. Quantitative measurements of T- and B-cell function in variable primary hypogammaglobulinemia: evidence for a consistent B-cell defect. Clin Exp Immunol. 1977; 27:208-15.
Ashman RF, Saxon A, Stevens RH. Profile of multiple lymphocyte functional defects in acquired hypogammaglobulinemia, derived from in vitro cell recombination analysis. J Allergy Clin Immunol. 1980; 65:242-56.
De Gast GC, Wilkins SR, Webster ADB, Rickinson A, Platts-Mills TAE. Functional immaturity of isolated B cells from patients with hypogammaglobulinemia. Clin Exp Immunol. 1980; 42:535-44.
Saiki O, Ralph P, Cunningham-Rundles C, Good RA. Three distinct stages of B-cell defects in common varied immunodeficiency. Proc Natl Acad Sci USA. 1982; 79:6008-12.
Bryant A, Calver NC, Toubi E, Webster ADB, Farrant J. Classification of patients with common variable immunodeficiency by B cell secretion of IgM and IgG in response to anti-IgM and interleukin-2. Clin Immunol Immunopathol. 1990; 56:239-48.
Kruger G, Welte K, Ciobanu N, Cunningham-Rundles C, Ralph P, Venuta S, et al. Interleukin-2 correction of defective in vitro T-cell mitogenesis in patients with common varied immunodeficiency. J Clin Immunol. 1984; 4:295-303.
Friedman JM, Fialkow PJ, Davis SD, Ochs HD, Wedgwood RJ. Autoimmunity in the relatives of patients with immunodeficiency diseases. Clin Exp Immunol. 1977; 28:375-88.
Schaffer FM, Palermos J, Zhu ZB, Barger BO, Cooper MD, Volanakis JE. Individuals with IgA deficiency and common variable immunodeficiency share polymorphisms of major histocompatibility complex class III genes. Proc Natl Acad Sci USA. 1989; 86:8015-9.
Sneller MC, Strober W. Abnormalities of lymphokine gene expression in patients with common variable immunodeficiency. J Immunol. 1990; 144:3762-9.
Grabstein KS, Dower S, Gillis S, Urdal D, Larsen A. Expression of interleukin 2 interferon- and IL 2 receptor by human peripheral blood lymphocytes. J Immunol. 1986; 136:4503-8.
Eisenstein EM, Jaffe J, Sneller MC, Stober W. Impaired and intact differentiation pathways in CD4 lymphocytes of patients with common variable immunodeficiency. J Allergy Clin Immunol. 1992; 89: 167.
Samelson LE, Patel MD, Weissman AM, Harford JB, Klausner RD. Antigen activation of murine T cells induces tyrosine phosphorylation of a polypeptide associated with the T cell antigen receptor. Cell. 1986; 46:1083-90.
Reth M. Antigen receptors on B lymphocytes. Annu Rev Immunol. 1992; 10:97-121.
Wright JJ, Wagner DK, Blaese RM, Hagengruber C, Waldmann TA, Fleisher TA. Characterization of common variable immunodeficiency: identification of patients with distinctive immunophenotypic and clinical features. Blood. 1990; 76:2046-51.
Phillips JH, Lanier LL. Lectin-dependent and anti-CD3 induced cytotoxicity are preferentially mediated by peripheral blood cytotoxic T lymphocytes expressing Leu-7 antigen. J Immunol. 1986; 136:1579-85.
Clement LT, Grossi CE, Gartland GL. Morphologic and phenotypic features of the subpopulation of Leu-2+ cells that suppress B cell differentiation. J Immunol. 1984; 133:2461-8.
Maher PC, O'Toole CM, Wreghitt TG, Spiegelhalter DJ, English TA. Cytomegalovirus infection in cardiac transplant recipients associated with chronic T cell subset ratio inversion with expansion of Leu-7+ TS-C+ subset. Clin Exp Immunol. 1985; 62:515-21.
Tomkinson BE, Wagner DK, Nelson DL, Sullivan JL. Activated lymphocytes during acute Epstein-Barr virus infection. J Immunol. 1987; 139:3802-7.
Carney WP, Iacoviello V, Hirsch MS. Functional properties of T lymphocytes and their subsets in cytomegalovirus mononucleosis. J Immunol. 1983; 130:390-3.
Gupta S. Abnormality of Leu2+ 7+ cells in acquired immune deficiency syndrome (AIDS), AIDS-related complex, and asymptomatic homosexuals. J Clin Immunol. 1986; 6:502-9.
Pantaleo G, De Maria A, Koenig S, Butini L, Moss B, Baseler M, et al. CD8+ T lymphocytes of patients with AIDS maintain normal broad cytolytic function despite the loss of human immunodeficiency virus-specific cytotoxicity. Proc Natl Acad Sci USA. 1990; 87:4818-22.
Jaffe J, Strober W, Sneller MC. Functional abnormalities of CD8 T cells define a unique subset of patients with common variable immunodeficiency. FASEB J. 1992; 6:A1120.
Grierson H, Purtilo DT. Epstein-Barr virus infections in males with the X-linked lymphoproliferative syndrome. Ann Intern Med. 1987; 106:538-45.
Sullivan JL, Byron KS, Brewster FE, Baker SM, Ochs HD. X-linked lymphoproliferative syndrome. Natural history of the immunodeficiency. J Clin Invest. 1983; 71:1765-78.
Sullivan JL. Epstein-Barr virus and lymphoproliferative disorders. Semin Hematol. 1988; 25:269-79.
Bruton OC. Agammaglobulinemia. Pediatrics. 1952; 9:722-8.
Janeway CA, Rosen FS. The globulins. IV. Therapeutic uses of globulin. N Engl J Med. 1966; 275:826-31.
Hill LE, Mollison PL. Conclusions. In: Hypogammaglobulinemia. Medical Research Council Special Report Series, no. 310, 1971.
Nolte MT, Pirofsky B, Gerritz GA, Golding B. Intravenous immunoglobulin therapy for antibody deficiency. Clin Exp Immunol. 1979; 36:237-43.
Ammann AJ, Ashman RF, Buckley RH, Hardie WR, Krantmann HJ, Nelson J, et al. Use of intravenous -globulin in antibody immunodeficiency: results of a multicenter controlled trial. Clin Immunol Immunopathol. 1982; 22:60-7.
Cunningham-Rundles C, Siegal FP, Smithwick EM, Lion-Boule A, Cunningham-Rundles S, O'Malley J, et al. Efficacy of intravenous gammaglobulin in primary humoral immunodeficiency disease. Ann Intern Med. 1984; 101:435-9.
Roifman CM, Lederman HM, Lavis S, Stein LD, Levison H, Gelfand EW. Benefit of intravenous IgG replacement in hypogammaglobulinemic patients with chronic sinopulmonary disease. Am J Med. 1985; 79:171-4.
Buckley RH, Schiff RI. The use of intravenous immune globulin in immunodeficiency disease. N Engl J Med. 1991; 325:110-7.
NIH consensus conference. Intravenous immunoglobulin. Prevention and treatment of disease. JAMA. 1990; 264:3189-93.
Cunningham-Rundles C. Intravenous immunoglobulin treatment in the primary immunodeficiency diseases. Immunol and Allergy Clinics of North America. 1988; 8:17-28.
Sperber KE, Mayer L. Gastrointestinal manifestations of common variable immunodeficiency. Immunol Allerg Clin North Am. 1988; 8:423-34.
Wright JJ, Birx DL, Wagner DK, Waldmann TA, Blaese RM, Fleisher TA. Normalization of antibody responsiveness in a patient with common variable immunodeficiency and HIV infection. N Engl J Med. 1987; 317:1516-20.
White WB, Ballow M. Modulation of suppressor-cell activity by cimetidine in patients with common variable hypoglobulinemia. N Engl J Med. 1985; 321:198-202.
Cunningham-Rundles C, Mayer L, Sapira E, Mendelsohn L. Restoration of immunoglobulin secretion in vitro in common variable immunodeficiency by in vivo treatment with polyethylene glycol-conjugated human recombinant interleukin-2. Clin Immunol Immunopathol. 1992; 64:46-56.