GORDON N. OLINGER, M.D.; MICHAEL E. KORNS, M.D.; LAWRENCE I. BONCHEK, M.D.
This content is PDF only. Please click on the PDF icon to access.
Aortic valvular insufficiency in Marfan's syndrome is ordinarily due to aortic dilatation (1). The aortic media shows degeneration of elastic fibers and replacement with mucopolysaccharide; the aortic valve usually lacks these findings, although leaflet redundancy, fenestration, and rupture are recognizable. Aortic pathology may be similar in the forme fruste of Marfan's where the noncardiovascular manifestations of mesodermal dystrophy are variable. Isolated myxomatous degeneration of the aortic valve is rare, however, and in the only three reported cases, perforations of valve leaflets caused insufficiency. (2, 3). We report herein the only known case of acute aortic insufficiency occurring without perforation in
OLINGER GN, KORNS ME, BONCHEK LI. Acute Aortic Valvular Insufficiency Due to Isolated Myxomatous Degeneration. Ann Intern Med. ;88:807–808. doi: 10.7326/0003-4819-88-6-807
Download citation file:
Published: Ann Intern Med. 1978;88(6):807-808.
Cardiology, Valvular Heart Disease.
Results provided by:
Copyright © 2019 American College of Physicians. All Rights Reserved.
Print ISSN: 0003-4819 | Online ISSN: 1539-3704
Conditions of Use